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Sjögren's syndrome in a child
European Journal of Pediatrics
|September 1, 1985
Insights
This case study highlights Sjögren
Area of Science:
- Pediatric Rheumatology
- Autoimmune Diseases
- Rare Childhood Conditions
Background:
- Sjögren's syndrome is rare in children, with the youngest previously reported case being a 5-year-old.
- Early diagnosis in pediatric patients is challenging due to atypical presentations.
Abstract:
Sjögren's syndrome is a relatively uncommon condition in the paediatric age group. The youngest child reported thus far was a 5-year-old girl. This article reports the case of a 2-year-old girl admitted for recurrent infections of the respiratory tract with diffuse pulmonary interstitial infiltrations and a progressive swelling of the parotid glands. The clinical features and the results of laboratory investigations, including parotid and hepatic biopsies, chest X-rays and sialography helped to establish the diagnosis of Sjögren's syndrome. Clinical, immunological and genetic characteristics of Sjögren's syndrome are reviewed.