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A 20-year review of ostium primum defect repair in children

American Heart Journal
|November 1, 1985
PubMed

Insights

Ostium primum defect repair in children shows low mortality and usually mild mitral insufficiency. However, significant arrhythmias are common, frequently requiring pacemaker implantation.

Area of Science:

  • Cardiology
  • Pediatric Cardiac Surgery

Background:

  • Ostium primum defects are a type of atrial septal defect.
  • Surgical repair is a common treatment for these defects in children.

Purpose of the Study:

  • To evaluate the long-term outcomes of ostium primum defect repair in a pediatric population.
  • To assess mortality, residual defects, mitral insufficiency, and arrhythmias after surgery.

Main Methods:

  • Retrospective review of 69 pediatric patients undergoing ostium primum defect repair between 1963 and 1983.
  • Follow-up ranged from 6 months to 20 years, with assessments via cardiac catheterization and noninvasive methods.

Main Results:

  • Low perioperative mortality (4/69).
  • Mitral insufficiency was mild to trivial in most patients (35/61), with severe insufficiency in 2.
  • Significant late arrhythmias occurred in 14/61 patients, with 8 requiring pacemakers.

Conclusions:

  • Ostium primum defect repair in children has a low mortality rate.
  • While mitral insufficiency is common, it is typically mild and nonprogressive.
  • Arrhythmias are a frequent and significant complication requiring intervention, including pacemaker implantation.

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