A Case of Anomalous Right Coronary Artery With Catastrophic Presentation
Farhana Anwar1, Ethan Hiles1, Maham Shahid1
1Internal Medicine, Health Corporation of America (HCA) Florida Orange Park Hospital, Orange Park, USA.
Insights
An anomalous right coronary artery (ARCA) takeoff from the left coronary cusp can cause sudden cardiac death. Prompt diagnosis and surgical correction, like coronary artery bypass grafting, are vital for favorable outcomes in young adults.
Area of Science:
- Cardiology
- Cardiovascular Surgery
- Medical Imaging
Background:
- Anomalous coronary arteries are rare but serious congenital heart defects.
- They increase the risk of myocardial ischemia, arrhythmias, heart failure, and sudden cardiac death (SCD).
- Early diagnosis and intervention are crucial for preventing catastrophic events.
Observation:
- A young male presented with sudden cardiac arrest due to anomalous right coronary artery (ARCA).
- Imaging revealed ARCA originating from the left coronary cusp with an inter-arterial course.
- The patient required multiple electrical cardioversions to restore normal sinus rhythm.
Findings:
- Cardiac catheterization and CT scan confirmed ARCA with an inter-arterial course.
- Surgical correction using coronary artery bypass grafting (CABG) was successfully performed.
- The patient experienced a full recovery and remained asymptomatic at two-year follow-up.
Implications:
- This case highlights the importance of prompt diagnosis of ARCA in young individuals presenting with cardiac arrest.
- Coronary artery bypass grafting is presented as an effective surgical option for ARCA, even in urgent scenarios.
- Successful surgical management can lead to long-term recovery and improved quality of life, preventing recurrent life-threatening events.
Abstract:
Anomalous coronary artery is a rare but potentially life-threatening alteration in the coronary vascular system that is related to an increased risk of myocardial ischemia, ventricular arrhythmias, heart failure, and sudden cardiac death (SCD). Here, we present the case of a young male who presented to the hospital after a witnessed sudden cardiac arrest. Bystander cardiopulmonary resuscitation was started immediately, and normal sinus rhythm was achieved after electrical cardioversion three times. He was admitted to the ICU for further care upon admission. A CT of the chest showed a potential vascular structure in between the aorta and the pulmonary trunk. He underwent cardiac catheterization, which identified minimal coronary artery disease with the anomalous takeoff of the right coronary artery from the left coronary cusp. A cardiac CT scan obtained also showed an anomalous right coronary artery (ARCA) with an inter-arterial course. After explaining available treatment options and obtaining informed consent, a surgical correction by cardiothoracic surgery was performed using the coronary artery bypass graft technique. The patient recovered well after the surgery and was discharged home. After two years of follow-up, he continued to live life normally without any symptoms. Early and accurate diagnosis of an anomalous coronary artery is imperative for timely intervention, as malignant coronary artery diseases can often have a catastrophic presentation with acute coronary syndromes, myocardial infarction, or SCD. We present here a case of successful diagnosis of ARCA and its prompt surgical correction using coronary artery bypass grafting technique in a young adult. Despite the availability of various other treatment options, our case underscores coronary artery bypass grafting as a viable choice for individuals with anomalous coronary arteries, particularly in urgent situations.
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