Thyroid Hormone Resistance: A 17-Year Follow-up Case Report

Cristina Giusto1, Marina Passeri1, Patrizia Sperti1

  • 1Division of Endocrinology and Diabetes, CTO Andrea Alesini Hospital, Department of Biomedicine and Prevention, University Tor Vergata, 00133, Rome, Italy.

Abstract

Insights

Resistance to thyroid hormone syndrome, often caused by TRβ gene mutations, presents varied symptoms. This case highlights long-term management of a patient with severe underweight, osteoporosis, and palpitations.

Area of Science:

  • Endocrinology
  • Genetics
  • Internal Medicine

Background:

  • Resistance to thyroid hormone (RTH) is a rare genetic disorder caused by mutations in thyroid hormone receptor genes, primarily Thyroid hormone Receptor-beta (TRβ).
  • Characterized by peripheral insensitivity to thyroid hormones, RTH leads to elevated thyroid hormone levels (FT3, FT4) with paradoxically non-suppressed Thyroid-stimulating Hormone (TSH).
  • Clinical manifestations range from hyperthyroid to hypothyroid symptoms, depending on the specific genetic mutation and receptor defect.

Observation:

  • A 24-year-old female diagnosed with RTH at age 7 presented with chronic headaches, palpitations, hyperhidrosis, frequent evacuations, and severe underweight.
  • Laboratory results confirmed high FT3 and FT4 levels with a non-suppressed TSH.
  • Complication screening revealed mild osteoporosis; cardiac function was normal, managed with bisoprolol.

Findings:

  • This case report details the long-term symptoms and complications associated with RTH syndrome.
  • The patient's prolonged history provides insights into the chronic effects and management challenges of RTH.
  • Observed complications included mild osteoporosis and significant underweight, alongside typical RTH hormonal profiles.

Implications:

  • This case underscores the importance of recognizing RTH as a rare but significant endocrine disorder.
  • Comprehensive evaluation and long-term monitoring are crucial for managing RTH complications like osteoporosis.
  • Understanding the diverse manifestations and progression of RTH aids in developing personalized treatment strategies.

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