[Xanthogranulomatous pyelonephritis in children and adults]

This report gives a review of the few known collections of cases in the world literature. There is an incidence of 6% and 25% in CPN and pyonephrosis respectively. Morphologic sign of XGP is a high degree of destruction of parenchyma and replacement by characteristic granuloma. The function of these kidneys is always markedly and irreversibly damaged. Comprehensive description of special pathologic anatomy, pathogenesis, diagnostics, and operative indication. We show two typical cases in adults, setting an example, and report about five own cases in children, after examining all nephrectomy specimens from 1968 to 1983. We present the age distribution in all reported cases in children and suggest a morphologic and topographic staging classification of XGP.