Right lung hypoplasia associated with polysplenia: A case report and literature review

Area of Science:

• Medical Imaging
• Radiology
• Congenital Abnormalities

Background:

• Pulmonary agenesis is a rare congenital lung malformation often diagnosed late in life.
• It can present with other congenital anomalies, including cardiac and gastrointestinal issues.
• Computed tomography (CT) aids in visualizing pulmonary and vascular structures.

Observation:

• A case of an adult male with dextroposition of the heart is presented.
• The patient was found to have a unilobed right lung.
• Associated polysplenia was also noted.

Findings:

• This specific combination of a unilobed right lung, dextroposition, and polysplenia in an adult is unprecedented in medical literature.
• CT imaging provided detailed anatomical insights.

Implications:

• This case expands the known spectrum of pulmonary agenesis presentations.
• It underscores the importance of advanced imaging like CT in diagnosing rare congenital conditions.
• Further research may elucidate the embryological links between these associated anomalies.