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Congenital cystic adenomatoid malformation in a toddler: Unusual presentation with pleural effusion
Radia Laanait1, Karima El Fakiri1, Noureddine Rada1
1Pediatric A Department, Mohammed VI University Hospital, Marrakesh, Morocco, Faculty of Medicine and Pharmacy, University Cadi Ayyad, Morocco.
Insights
Congenital cystic adenomatoid malformation (CCAM) is a rare lung lesion. This case highlights CCAM presenting as pleural effusion in an infant, successfully treated with surgery.
Area of Science:
- Pediatric Pulmonology
- Thoracic Surgery
- Medical Imaging
Background:
- Congenital cystic adenomatoid malformation (CCAM) involves abnormal lung development, typically diagnosed in early childhood.
- CCAM presents with diverse clinical and radiological features, often requiring surgical intervention.
Observation:
- A 15-month-old boy presented with acute respiratory distress due to pleural effusion.
- Chest CT scan identified a cystic lesion in the right lower lobe, consistent with CCAM.
Findings:
- Surgical excision confirmed CCAM Type 1 without malignancy.
- Post-operative recovery was uneventful with no recurrence during 8-month follow-up.
Implications:
- Early diagnosis of CCAM is critical for timely intervention and improved outcomes in infants.
- Enhanced awareness among pediatricians and radiologists can facilitate prompt management of this rare congenital anomaly.
Abstract:
Congenital cystic adenomatoid malformation encompasses a series of cystic malformative lesions characterized by aberrant bronchiolar formations of varying size and dispersion. Most cases of this illness are detected in the first few years of life, usually affecting infants. We report a case of CCAM presenting as pleural effusion in a 15-month-old boy who presented with acute respiratory distress. Chest CT revealed a cystic image in the right lower lobe of the lung. The patient had surgical excision, and a pathological examination validated the diagnosis of CCAM type 1 with no malignant material. Following surgery, the patient's general condition improved, and no new respiratory symptoms were observed during an 8-month follow-up period. Increased awareness of this rare condition among pediatricians and radiologists is crucial for facilitating early diagnosis and appropriate treatment.
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