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Electric storm triggered by short-coupled premature ventricular complexes in a young patient with non-obstructive

Ngoda Manongi1, Lior Jankelson2, Daniele Massera3

  • 1Division of Cardiology, NewYork-Presbyterian Queens, Flushing, New York, USA nmanongi@gmail.com.

BMJ Case Reports
|September 21, 2024
PubMed

Insights

Ventricular arrhythmias, a feared complication of hypertrophic cardiomyopathy, can lead to electrical storms. This case highlights a young patient with non-obstructive hypertrophic cardiomyopathy experiencing a refractory electrical storm.

Area of Science:

  • Cardiology
  • Electrophysiology
  • Genetics

Background:

  • Hypertrophic cardiomyopathy (HCM) is a genetic heart muscle disease.
  • Ventricular arrhythmias, including ventricular tachycardia, are a significant concern in HCM.
  • Electrical storms, characterized by recurrent ventricular arrhythmias, portend a poor prognosis.

Observation:

  • A young patient with non-obstructive hypertrophic cardiomyopathy presented with syncope.
  • The patient experienced an electrical storm, a severe manifestation of ventricular arrhythmias.
  • The electrical storm was refractory to standard medical management.

Findings:

  • Non-obstructive hypertrophic cardiomyopathy can precipitate life-threatening ventricular arrhythmias.
  • Electrical storms in HCM, even in younger patients, pose a significant clinical challenge.
  • Refractory electrical storms necessitate consideration of advanced therapeutic strategies.

Implications:

  • This case underscores the importance of vigilant arrhythmia monitoring in HCM patients.
  • Early recognition and aggressive management of electrical storms are crucial for improving outcomes.
  • Further research into novel therapeutic approaches for refractory ventricular arrhythmias in HCM is warranted.

Keywords:
ArrhythmiasCardiovascular systemHeart failurePacing and electrophysiology

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