Case Report: A "senior" with serpentine-like syndrome-treatment of combined brachyoesophagus, intrathoracic stomach and cervical rachischisis
View abstract on PubMed
Summary
This summary is machine-generated.Serpentine-like syndrome, a rare condition, presents significant challenges. This case highlights a patient surviving to age five, offering insights into managing this complex congenital disorder.
Area Of Science
- Pediatric Surgery
- Medical Genetics
- Congenital Malformations
Background
- Serpentine-like syndrome (SLS) is a rare congenital disorder identified in 2008.
- SLS is characterized by intrathoracic stomach, short esophagus, splenic abnormalities, and cervical spine malformations.
- The syndrome is associated with a high mortality rate.
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