Cine-computed tomography of arrhythmogenic right ventricular dysplasia

The CT diagnostic features of arrhythmogenic right ventricular dysplasia (Uhl anomaly) are described in a 72-year-old man. High speed cine-CT was performed using millisecond exposures and multilevel scanning. Ventricular morphology and function were evaluated, and findings were compared with two-dimensional echocardiography and equilibrium gated blood pool imaging. Cine-CT showed a dilated hypokinetic right ventricle with a markedly thin anterior wall and normal left sided chambers. The clinical aspects of Uhl anomaly are reviewed.