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Quadricuspid aortic valve with complete heart block: a double whammy
Mukesh Dhillon1, Aditi Sharma2
1Department of Medicine, Command Hospital, Panchkula, India. drdhillon189@gmail.com.
A rare quadricuspid aortic valve (QAV) coexisted with complete heart block (CHB) in a young male. This extremely rare congenital heart disease combination requires careful patient evaluation and monitoring.
Area of Science:
- Cardiology
- Congenital Heart Disease
Background:
- Bicuspid aortic valve is the most common congenital heart disease.
- Quadricuspid aortic valve (QAV) is an exceedingly rare abnormality.
Purpose of the Study:
- To report a rare case of QAV coexisting with complete heart block (CHB).
- To highlight the rarity of this specific congenital heart disease combination.
Main Methods:
- Case report of a young male presenting with syncope.
- Diagnostic evaluation including echocardiography.
- Successful permanent pacemaker implantation.
Main Results:
- Diagnosis of QAV and CHB in a young male.
- This QAV and CHB combination, without prior surgery or endocarditis, is exceptionally rare, with only one prior report.
- Patient underwent successful pacemaker implantation and is monitored for aortic regurgitation.
Conclusions:
- The coexistence of QAV and CHB is extremely rare, especially without infective endocarditis or aortic valve surgery.
- This rare condition necessitates thorough patient evaluation and long-term follow-up.
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