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Published on: August 30, 2022
Granulomatosis With Polyangiitis Causing Severe Aortic Regurgitation
Katarina L Fabre1, Megan Ellis1, Katlin T Schmitz1
1Department of Internal Medicine, Mayo Clinic, Rochester, Minnesota, USA.
Abstract:
Cardiac granulomatosis with polyangiitis is a rare necrotizing vasculitis impacting small to medium vessels. We present a case of granulomatosis with polyangiitis causing acute aortic valve regurgitation. Imaging reveals valve thickening, inflammation without destruction. Treatment involves glucocorticoids and rituximab for remission, with consideration of surgery for severe valve disease.
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