Giant aggressive angiomyxoma of the vulva in two women

Aggressive angiomyxoma (AA) of the vulva is a rare, benign, slow-growing tumour that arises from the myxoid cells of the connective tissue. It has a low tendency to metastasise, but a high chance of multiple local recurrences. Here, we report two cases of AA of the vulva. In both these cases, women in the reproductive age group presented with the condition of a large, fleshy, pedunculated mass on the labia majora. The mass was surgically resected and sent for histopathology, which confirmed the diagnosis. AA should be kept as one of the differential diagnoses for a vulvovaginal mass. Its correct diagnosis, optimal treatment and long-term follow-up are necessary for appropriate management of such patients.