Pseudotumoral portal cavernoma: A rare case that challenges diagnosis

Portal cavernoma cholangiopathy (PCC), also known as portal biliopathy, refers to biliary duct abnormalities caused by extrahepatic portal vein obstruction (EHPVO) and subsequent cavernous transformation of the portal vein. Pseudotumoral portal cavernoma is a specific subtype of PCC characterized by the presence of numerous thin collateral veins that mimic the sheath of the common bile duct (CBD). We present a case of a 42-year-old women with pseudotumoral portal cavernoma secondary to portal vein thrombosis, a complication of myeloproliferative disorder. This case underscores the diagnostic challenges posed by pseudotumoral portal cavernoma and emphasizes the crucial role of imaging in achieving an accurate diagnosis.