Primary intracranial myoepithelioma in a child

Myoepitheliomal tumours, associated with the salivary glands and certain soft tissue sites, are unusually encountered in the central nervous system (CNS). In the brain, although the most common location is the Sella, other areas can infrequently be involved. Such intracranial lesions are exceptionally rare in children. We report a case of CNS myoepithelioma in a child harbouring an intra-axial posterior frontal mass and briefly review the relevant literature. This 8-year-old-boy presenting with features of intracranial pressure effects underwent excision of the lesion, and the diagnosis was confirmed with histopathology and immunohistochemical studies. He had a good clinical outcome. Unusually, primary intracranial myoepitheliomas can manifest as cerebral parenchymal mass lesions. Although these are usually a pathological surprise, the index case and available limited reports highlight the need for an awareness of such uncommon paediatric tumours, both in an intra-axial and dural location.