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Neuralgic amyotrophy with hourglass-like constrictions: A case report
Mi-Hyeon Bang1, Ha-Lim Song1, Seok Hahn2
1Department of Physical Medicine and Rehabilitation, Haeundae Paik Hospital, Inje University College of Medicine, Busan 48108, South Korea.
World Journal of Clinical Cases
|December 9, 2024
Summary
Neuralgic amyotrophy (NA) presents with sudden arm pain and weakness. Unique features like hourglass-like focal constriction aid diagnosis, differentiating it from cervical radiculopathy.
Area of Science:
- Neurology
- Medical Diagnostics
Background:
- Neuralgic amyotrophy (NA) is a rare neurological disorder characterized by sudden upper limb pain and subsequent muscle weakness.
- It typically affects the brachial plexus, but rare paraspinal muscle involvement can mimic cervical radiculopathy.
Observation:
- A 76-year-old male with hip pain post-fall developed sudden left shoulder pain and arm weakness after surgery.
- Initial imaging suggested cervical disc bulging, but electrodiagnostic studies indicated brachial plexopathy.
- Magnetic resonance neurography revealed brachial plexus inflammation and a characteristic suprascapular nerve hourglass-like focal constriction (HLFC).
Findings:
- The patient was diagnosed with NA based on clinical presentation and imaging findings, including HLFC.
- Treatment involved corticosteroids and physical therapy, leading to significant improvement in shoulder muscle strength.
Implications:
- Recognizing unique NA features, such as HLFC and potential paraspinal involvement, is vital for accurate diagnosis.
- Distinguishing NA from cervical radiculopathy prevents misdiagnosis and ensures appropriate treatment.
- This case highlights the utility of advanced imaging in diagnosing rare neurological conditions.
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