A Rare Case of Extralobar Bronchopulmonary Sequestration

Bronchopulmonary sequestration is a rare developmental abnormality of the pulmonary system. It is a pulmonary malformation and is defined as lung tissue without connection to the tracheobronchial tree with a systemic blood supply. We present a case of an eight-month-old infant with prenatally diagnosed bronchopulmonary sequestration. At six months of age, an extralobar sequestration with a feeding vessel from truncus coeliacus and venous drainage to vena thoracica interna sinistra was diagnosed from a CT scan of the lung. Thoracoscopy was performed with the identification of intradiaphragmatic sequestration, conversion to thoracotomy with resection of the lesion, and repair of the diaphragm. Postoperative follow-up revealed no complications. Intradiaphragmatic bronchopulmonary sequestration is an extremely rare congenital anomaly. The gold standard for diagnostic clarification is computed tomography. The preferred approach for surgical treatment is transthoracic.