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Updated: Jun 5, 2025
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Systematic Hearing Performance Evaluation Process for Adolescents with Cochlear Implantation at Early Ages
Published on: March 24, 2023
336
Hearing implants in pediatrics with cochlear nerve deficiency: an updated systematic review
Asma Alahmadi1, Yassin Abdelsamad2, Nouf A AlAmari3
1King Abdullah Ear Specialist Center (KAESC), College of Medicine, King Saud University, Riyadh, Saudi Arabia.
Summary
Cochlear nerve deficiency (CND) management options like cochlear implants (CI) show variable outcomes. Auditory brainstem implants (ABI) offer a promising alternative for improved auditory and speech results in CND patients.
Area of Science:
- Otolaryngology
- Neuroscience
- Genetics
Background:
- Cochlear nerve deficiency (CND) causes significant congenital hearing loss.
- Cochlear implantation (CI) and auditory brainstem implantation (ABI) are primary CND management strategies.
- Limited evidence exists on the comparative effectiveness of CND interventions.
Purpose of the Study:
- To systematically review and assess the effectiveness of various management approaches for CND.
- To update the evidence base on outcomes for CI and ABI in CND.
- To identify optimal treatment strategies for congenital hearing loss due to CND.
Main Methods:
- A comprehensive literature search was performed across PubMed, Scopus, Web of Science, and CENTRAL.
- Included studies encompassed interventional and observational designs evaluating CND management.
- Data synthesis focused on auditory, speech, and learning outcomes.
Main Results:
- Twenty-five studies were analyzed, including retrospective and prospective designs.
- Most studies focused on children with cochlear nerve aplasia or hypoplasia.
- Outcomes for both CI and ABI were variable, with ABI showing promise.
Conclusions:
- Cochlear implantation is a feasible option for CND but has limited effectiveness in some cases.
- Auditory brainstem implantation emerges as a promising alternative for CND.
- ABI may offer superior auditory, speech, and learning outcomes compared to CI in CND.
