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Defective [U-14 C] palmitic acid oxidation in Duchenne muscular dystrophy
Neurology
|January 1, 1985
Abstract:
Compared with normal skeletal muscle, muscle from patients with Duchenne dystrophy had decreased [U-14 C] palmitic acid oxidation. [1-14 C] palmitic acid oxidation was normal. These results may indicate a defect in intramitochondrial fatty acid oxidation.