Primary Cardiac Leiomyosarcoma Extending From Right Atrium to Inferior Vena Cava Without Metastasis: A Case Report

Jennifer Chong1, Tanya Richvalsky2, Sridhar Musuku2

  • 1Cardiothoracic Surgery, Albany Medical Center, Albany, USA.

Cureus
|December 17, 2024
PubMed

Insights

A rare intracardiac mass, identified as high-grade leiomyosarcoma, was successfully excised in a patient with a history of acute lymphoblastic leukemia. This case highlights the surgical management of rare cardiac tumors.

Area of Science:

  • Cardiovascular Surgery
  • Oncology
  • Radiology

Background:

  • A 27-year-old female with a history of acute lymphoblastic leukemia in remission presented with concerning symptoms.
  • Initial investigations revealed hepatic vein thrombosis and cirrhosis, prompting further imaging.
  • Computed tomography (CT) and magnetic resonance imaging (MRI) identified a significant intracardiac mass.