Complete Clinical Recovery Following Surgical Excision of Extensive Primary Cardiac Sarcoma

Primary cardiac tumors are rare, most of them being benign. Most malignant cardiac tumors are sarcomas, with the most important therapeutic option being surgery, along with perioperative chemo- and radiotherapy. Here, we present a case of a 67-year-old female patient with no prior medical condition, who presented with primary cardiac sarcoma and extensive tumor growth in the pulmonary artery. Debulking of the tumor mass was performed, along with pulmonary valve replacement, tricuspid valve reconstruction, and patent foramen ovale closure. This was followed by adjuvant radiotherapy. The patient remains in remission with an excellent clinical status after 18 months. Despite surgery, previous register studies on cardiac sarcomas have reported a median survival that typically does not exceed 2 years. Given this poor prognosis, surgical therapy is sometimes not carried out. Despite this, in our case, surgical tumor debulking in combination with radiotherapy relieved symptoms and the patient is in good health 18 months later.