Related Concept Videos
Venous Thrombosis III: Interprofessional Care
Anticoagulant Drugs: Low-Molecular-Weight Heparins
Clot Retraction and Fibrinolysis
Disorders of Hemostasis
Thromboembolic Disorders
Two factors primarily cause thromboembolic conditions.
Pulmonary Embolism II: Diagnostic Studies and Interprofessional Care
You might also read
Related Articles
Articles linked to this work by shared authors, journal, and citation graph.
A novel FGG missense variant associated with fibrinogen storage disease in a large family from Quebec.
Related Experiment Video
Updated: Jun 12, 2025

Measurement of Factor V Activity in Human Plasma Using a Microplate Coagulation Assay
Published on: September 9, 2012
How I treat quantitative fibrinogen disorders.
1Division of Angiology and Hemostasis, University Hospitals of Geneva, Geneva, Switzerland; and Department of Medicine, Faculty of Medicine, University of Geneva, Geneva, Switzerland.
Quantitative fibrinogen disorders, like afibrinogenemia and hypofibrinogenemia, involve low or absent fibrinogen. Management of bleeding, thrombosis, surgery, and pregnancy requires careful fibrinogen replacement and thromboprophylaxis strategies.
Area of Science:
- Hematology
- Genetics
- Clinical Medicine
Background:
- Quantitative fibrinogen disorders (afibrinogenemia, hypofibrinogenemia) are monogenic conditions characterized by absent or reduced fibrinogen.
- Severity correlates with fibrinogen levels, impacting bleeding risk from mild to life-threatening.
- These disorders present unique challenges in managing bleeding, thrombosis, surgery, and pregnancy.
Purpose of the Study:
- To present clinical scenarios illustrating common challenges in managing quantitative fibrinogen disorders.
- To propose evidence-based strategies for addressing bleeding, thrombosis, surgical interventions, and pregnancy in affected individuals.
Main Methods:
- Diagnosis relies on measuring fibrinogen activity and antigen levels.
- Case-based approach presenting 4 distinct clinical scenarios.
- Review of current literature and clinical guidelines for management strategies.
Main Results:
- Afibrinogenemia typically involves severe bleeding, while hypofibrinogenemia ranges from asymptomatic to mild bleeding.
- A prothrombotic tendency exists, potentially worsened by fibrinogen supplementation.
- Management requires tailored fibrinogen replacement and thromboprophylaxis, especially during surgery and pregnancy.
Conclusions:
- Effective management of quantitative fibrinogen disorders necessitates a comprehensive approach addressing bleeding, thrombosis, and specific life events.
- Clinical scenarios highlight the complexity and need for individualized treatment strategies.
- Further research may refine optimal therapeutic protocols for these rare conditions.

