Benign Yellow Dot Maculopathy: A Case Series of Patients With a Recently Discovered Macular Phenotype

Benign yellow dot maculopathy (BYDM) is a recently described rare, asymptomatic, early onset, and non-progressive macular phenotype. It is characterized by the presence of multiple white-yellow dots encircling the fovea, which are hyperautofluorescent on fundus autofluorescence. Here, we expand on the few reports available by presenting a case series of five Portuguese patients with clinical BYDM phenotype and congruent multimodal imaging, including the second reported unilateral case. All five patients were female, with a mean age of 31 ± 16 years and mean visual acuity of 0.04 logMAR (logarithm of the minimum angle of resolution), which remained stable throughout long-term follow-up.