Anomalous left pulmonary artery: case reports exploring anatomic variants
Yibei Zhu1, Olivia McCloskey1, Justin A Robinson2
1Case Western Reserve University School of Medicine, Cleveland, OH, USA.
Insights
Pulmonary artery sling (PAS) is a rare congenital anomaly affecting infants. Surgical correction of anomalous left pulmonary artery (LPA) anatomy is vital for relieving airway compression and improving respiratory function.
Area of Science:
- Pediatric Surgery
- Thoracic Surgery
- Congenital Heart Disease
Background:
- Pulmonary artery sling (PAS) is a rare congenital anomaly.
- It involves the left pulmonary artery (LPA) originating abnormally, compressing the trachea and esophagus.
- This compression frequently causes severe respiratory distress in infants.
Background:
Pulmonary artery sling (PAS) is a rare congenital anomaly where the left pulmonary artery (LPA) branches from the right pulmonary artery, compressing the trachea and esophagus and frequently leading to respiratory distress in infants. Surgical intervention, such as LPA reimplantation or translocation, is crucial to relieve airway compression and restore normal pulmonary function.
Case Presentation:
This report highlights varied LPA anatomies, including a unique case of an anomalous LPA without true sling formation but causing tracheal compression, alongside two typical PAS cases. Respiratory symptoms were successfully mitigated in all three cases without concomitant tracheal reconstruction.
Conclusions:
This report underscores the necessity of thorough preoperative assessment of airway anatomy and highlight the importance of individualized surgical planning for anomalous LPA.
