Cavoatrial Bypass for Cardiac Complications From Rosai-Dorfman Disease
Quynh Nguyen1, Rachel Bourke2,3, Richard W Gilbert3,4
1Division of Cardiac Surgery, University of British Columbia, Vancouver, British Columbia, Canada.
Annals of Thoracic Surgery Short Reports
|January 10, 2025
Abstract:
Rosai-Dorfman disease (RDD) is a nonmalignant disease of histiocyte proliferation. RDD usually presents with painless cervical lymphadenopathy, although extranodal involvement can occur. Cardiac involvement was reported in <0.1% of cases. We present a case of cardiac RDD with obstruction at the inferior vena cava-right atrial junction.


