[Idiopathic pulmonary arterial hypertension revealed by right ventricular dysfunction]

Valérie Bartsch1, Fanny Gester2, Gilles Parzibut2

  • 1Service de Pédiatrie, CHU Liège, Belgique.

Revue Medicale De Liege
|January 16, 2025
PubMed
Summary

Idiopathic pulmonary arterial hypertension (iPAH) is a rare disease causing high mortality. Vasoreactivity testing during catheterization is crucial for identifying patients who may benefit from calcium channel blockers, improving pulmonary hemodynamics.

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