IgG4-RD-Associated Mikulicz Syndrome Without Classic Systemic Involvement-A Case Report

Luis Ángel Mendoza-Vargas1, Samuel Sevilla-Fuentes1, Brandon Bautista-Becerril2,3

  • 1Hospital General de Zona 1 "Emilio Varela Luján", Zacatecas 98000, Mexico.

PubMed
Summary

This case study shows that IgG4-related disease (IgG4-RD) can occur with normal IgG4 levels, emphasizing histopathology for diagnosis. Early steroid treatment led to significant symptom resolution and recovery.

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