Insights

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital heart defect. Early diagnosis and surgical correction are critical to prevent high infant mortality rates.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Medical Imaging

Background:

  • Congenital heart disease impacts approximately 1% of newborns annually.
  • Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare condition, accounting for 0.25%-0.50% of congenital cardiac diseases.
  • Untreated ALCAPA has a mortality rate as high as 90% in infants.

Purpose of the Study:

  • To report a case of ALCAPA in an infant presenting with respiratory illness.
  • To highlight the diagnostic utility of echocardiography and CT angiography in ALCAPA.
  • To emphasize the importance of timely surgical intervention and post-operative care.

Main Methods:

  • Case report of a 4-month-old infant.
  • Diagnostic imaging included chest radiography, echocardiography, and gated computed tomography angiography (CTA).
  • Surgical correction and post-operative circulatory support were performed.

Main Results:

  • The infant presented with cardiomegaly and severe left ventricular dysfunction.
  • Echocardiography suggested ALCAPA, which was confirmed by CTA.
  • Successful surgical correction and recovery with circulatory support were achieved.

Conclusions:

  • ALCAPA is a critical congenital heart defect requiring prompt diagnosis and management.
  • Multimodality imaging plays a vital role in diagnosing ALCAPA.
  • Urgent surgical repair and appropriate post-operative care are essential for favorable outcomes in ALCAPA patients.

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