Primary Mediastinal Synovial Sarcoma with Pericardial Involvement: A Case Report
Kenan C Michaels1, Sean C Dougherty2, Brett R Kurpiel3
1Department of Medicine, University of Virginia Medical Center, Charlottesville, VA, USA.
Case Reports in Oncology
|February 21, 2025
Summary
This case highlights a rare mediastinal synovial sarcoma presenting as recurrent pericardial effusion in a young adult. Early diagnosis with advanced imaging is crucial for this aggressive soft tissue sarcoma.
Area of Science:
- Oncology
- Pathology
- Cardiology
Background:
- Synovial sarcoma is a rare soft tissue sarcoma, typically affecting young adults in the extremities.
- Mediastinal synovial sarcoma is exceptionally rare and can present insidiously.
- Malignant pericardial effusion can be the primary manifestation of mediastinal synovial sarcoma.
Keywords:
Adolescent and young adultCardiac magnetic resonance imagingNext-gen sequencingPericardial effusionPrimary mediastinal synovial sarcomaMore Related Videos
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