Predicting the structure-altering mechanisms of disease variants
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Updated: May 24, 2025

In Vivo Functional Study of Disease-associated Rare Human Variants Using Drosophila
Published on: August 20, 2019
Matteo Arnaudi1, Mattia Utichi1, Matteo Tiberti2
1Cancer Structural Biology, Danish Cancer Institute, Strandboulevarden 49, 2100, Copenhagen, Denmark; Cancer Systems Biology, Section of Bioinformatics, Health and Technology Department, Technical University of Denmark, Lyngby, Denmark.
Abstract:
Missense variants can affect the severity of disease, choice of treatment, and treatment outcomes. While the number of known variants has been increasing at a rapid pace, available evidence of their clinical effect has been lagging behind, constituting a challenge for clinicians and researchers. Multiplexed assays of variant effects (MAVEs) are important to close the gap; nonetheless, computational predictions of pathogenicity are still often the only available data for scoring variants. Such methods are not designed to provide a mechanistic explanation for the effect of amino acid substitutions. To this purpose, we propose structure-based frameworks as ensemble methodologies, with each method tailored to predict a different aspect among those exerted by amino acid substitutions to link predicted pathogenicity to mechanistic indicators. We review available frameworks, as well as advancements in underlying structure-based methods that predict variant effects on several protein features, such as protein stability, biomolecular interactions, allostery, post-translational modifications, and more.
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