Case Report on Rhabdomyosarcoma of Middle Ear in A 4 Year Old Child: A Rare Case

Shyamji Rawat1, Preeti Solanki1, Lalit Mohan Patel1

  • 1State Cancer Institute, Netaji Subhash Chandra Bose Medical College, Jabalpur, Madhya Pradesh India.

Insights

Embryonal rhabdomyosarcoma, a rare childhood cancer, can present as chronic ear infections. Early biopsy is crucial for children with persistent or worsening ear issues unresponsive to treatment.

Area of Science:

  • Pediatric Oncology
  • Otolaryngology
  • Soft Tissue Sarcomas

Background:

  • Rhabdomyosarcoma is the most common childhood soft tissue sarcoma, often affecting the head and neck.
  • Malignancies in the ear and temporal regions are rare but present diagnostic challenges.
  • Chronic otitis media (CSOM) is a common pediatric condition, potentially masking other pathologies.

Purpose of the Study:

  • To highlight embryonal rhabdomyosarcoma as a rare but critical differential diagnosis in pediatric CSOM.
  • To emphasize the importance of considering rhabdomyosarcoma in non-responsive or worsening ear infections.
  • To advocate for prompt histopathologic evaluation in suspicious cases.

Main Methods:

  • Case report of a 4-year-old boy with a right external auditory canal mass and facial deviation.
  • Initial symptomatic treatment for presumed otitis media.
  • Referral for persistent purulent discharge, leading to histopathologic diagnosis of embryonal rhabdomyosarcoma.

Main Results:

  • The patient was diagnosed with embryonal rhabdomyosarcoma after presenting with symptoms mimicking chronic otitis media.
  • The tumor manifested as a mass in the external auditory canal with associated facial nerve involvement.
  • Histopathologic evaluation confirmed the diagnosis.

Conclusions:

  • Rhabdomyosarcoma must be considered in the differential diagnosis of pediatric chronic otitis media.
  • Children with CSOM unresponsive to medical management or showing disease progression warrant further investigation.
  • Biopsy is essential for accurate diagnosis and timely treatment initiation in suspected cases.