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Improving Inpatient Cystic Fibrosis Exacerbation Care: A Resident Physician Training Approach
Roger Auth1, Sarah Rhoads2, Michael Blundin1
1Department of Medicine, Division of Pulmonary and Critical Care and Sleep, The Warren Alpert Medical School of Brown University, Providence, RI.
Background:
Novel therapies have increased life expectancy for people with cystic fibrosis (pwCF), shifting care to adult providers with limited CF experience. Hospitalizations expose trainees to CF care, but educational tools for managing CF exacerbations are scarce.
Methods:
A six-year longitudinal study assessed internal medicine resident physician trainees' (RPTs) experience managing hospitalized pwCF. A mixed-method survey of RPTs informed the creation of educational and workflow tools, including a video didactic and order set. A targeted knowledge assessment measured the effectiveness of these tools. Multidisciplinary team meetings also tracked challenges and outcomes.
Results:
Among 48 RPTs surveyed, 83% cared for pwCF during training. Most reported less comfort managing pwCF compared to diseases like chronic obstructive pulmonary disease (COPD). Immediately after implementing targeted educational tools, knowledge scores improved, particularly in CF-related diabetes management (38.4% correct pre vs 61.5% correct post, p=0.04).
Conclusion:
Rare disease education requires focused assessments of learners' needs, sustained reinforcement, and adaptable tools to maintain effectiveness.
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