IVCA in a Boy with Multilocular Renal Cyst as a Risk Factor for Deep Vein Thrombosis

Agnieszka Szmigielska1, Piotr Skrzypczyk1, Michał Szyszka1

  • 1Department of Pediatrics and Nephrology, Medical University of Warsaw.

PubMed

Insights

KILT syndrome involves kidney defects, congenital inferior vena cava agenesis (IVCA), and leg deep vein thrombosis. Early detection of IVCA is crucial for preventing dangerous thrombotic complications.

Area of Science:

  • Vascular Surgery
  • Nephrology
  • Radiology

Background:

  • KILT syndrome is characterized by renal defects, congenital inferior vena cava agenesis (IVCA), and lower limb deep vein thrombosis.
  • Congenital IVCA is a rare vascular anomaly that can lead to significant clinical complications.
Abstract

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