Criss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia

Hongqin Liang1, Li Kong2, Fei Liu3

  • 1Department of Radiology, Third Military Medical University Southwest Hospital (Army Medical University), Chongqing, China.

PubMed

Insights

Criss-cross heart (CCH) is a rare congenital heart defect. This case highlights a unique CCH presentation with situs inversus totalis and bronchial dysplasia, emphasizing CT angiography

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Criss-cross heart (CCH) is a rare congenital heart malformation.
  • CCH involves twisted atrioventricular connections and is often associated with other cardiac anomalies.
  • Accurate diagnosis of CCH can be challenging due to its complexity.

Purpose of the Study:

  • To report a previously undocumented case of CCH with complex associated malformations.
  • To illustrate the diagnostic utility of CT angiography in such complex cases.
  • To discuss the implications for surgical planning and treatment.

Main Methods:

  • Case presentation of a 10-year-old girl with recurrent cyanosis and fatigue.
  • Echocardiography identified CCH, dextrocardia, pulmonary hypertension, VSD, ASD, and PDA.
  • CT angiography revealed bronchial dysplasia and double-outlet right ventricle (DORV).

Main Results:

  • The patient presented with a rare combination of CCH, mirror dextrocardia, situs inversus totalis, and bronchial dysplasia.
  • CT angiography proved essential for a comprehensive assessment of the complex cardiac and non-cardiac anomalies.
  • The findings underscore the importance of advanced imaging in managing complex congenital heart disease.

Conclusions:

  • CCH is a rare condition with complex associated anomalies, posing diagnostic challenges.
  • CT angiography is crucial for detailed evaluation and surgical planning in CCH.
  • This unique case emphasizes the role of CT in guiding treatment for complex congenital heart defects, though further research on surgical strategies is needed.
Abstract

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