Criss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia
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Published on: February 11, 2022
Hongqin Liang1, Li Kong2, Fei Liu3
1Department of Radiology, Third Military Medical University Southwest Hospital (Army Medical University), Chongqing, China.
Insights
Criss-cross heart (CCH) is a rare congenital heart defect. This case highlights a unique CCH presentation with situs inversus totalis and bronchial dysplasia, emphasizing CT angiography
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Criss-cross heart (CCH) is a rare congenital heart malformation.
- CCH involves twisted atrioventricular connections and is often associated with other cardiac anomalies.
- Accurate diagnosis of CCH can be challenging due to its complexity.
Purpose of the Study:
- To report a previously undocumented case of CCH with complex associated malformations.
- To illustrate the diagnostic utility of CT angiography in such complex cases.
- To discuss the implications for surgical planning and treatment.
Main Methods:
- Case presentation of a 10-year-old girl with recurrent cyanosis and fatigue.
- Echocardiography identified CCH, dextrocardia, pulmonary hypertension, VSD, ASD, and PDA.
- CT angiography revealed bronchial dysplasia and double-outlet right ventricle (DORV).
Main Results:
- The patient presented with a rare combination of CCH, mirror dextrocardia, situs inversus totalis, and bronchial dysplasia.
- CT angiography proved essential for a comprehensive assessment of the complex cardiac and non-cardiac anomalies.
- The findings underscore the importance of advanced imaging in managing complex congenital heart disease.
Conclusions:
- CCH is a rare condition with complex associated anomalies, posing diagnostic challenges.
- CT angiography is crucial for detailed evaluation and surgical planning in CCH.
- This unique case emphasizes the role of CT in guiding treatment for complex congenital heart defects, though further research on surgical strategies is needed.
Background:
Criss-cross heart (CCH) is a rare congenital heart malformation characterized by twisted atrioventricular connections, often associated with various other cardiac anomalies, making accurate diagnosis challenging; In this article, we present a previously unreported case of CCH with complex cardiac malformation, situs inversus totalis, and bronchial dysplasia.
Case Presentation:
A 10-year-old girl presented with recurrent cyanosis and fatigue, and echocardiography revealed a complex congenital heart condition involving CCH, dextrocardia, severe pulmonary hypertension, ventricular septal defect (VSD), atrial septal defect (ASD), and patent ductus arteriosus (PDA). Further CT angiography unveiled bronchial dysplasia and double-outlet right ventricle (DORV).
Conclusions:
CCH is a rare congenital heart condition characterized by twisted atrioventricular connections, with complex associated anomalies. Diagnosis is challenging due to the variety of defects. CT angiography is crucial for comprehensive assessment and surgical planning. This case presented a unique combination of CCH with mirror dextrocardia, situs inversus totalis, and bronchial malformation, highlighting the importance of CT in guiding treatment decisions. However, postoperative follow-up is lacking, and optimal surgical strategies for such complex deformities remain to be explored.
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