A case of left main coronary artery to pulmonary fistula associated with vasospastic angina
Kentaro Shirakura1, Shougo Takahashi1, Kaname Shimizu1
1Department of Cardiac Surgery, Asahikawa Medical University, Midorigaoka Higashi 2-1-1-1, Asahikawa 078-8510, Japan.
Insights
Coronary artery fistulas (CAFs) can cause myocardial ischemia. This case highlights that CAFs may also trigger vasospasm, a complication potentially missed during preoperative diagnostics for coronary artery-pulmonary artery fistulas.
Area of Science:
- Cardiology
- Cardiac Surgery
- Vascular Medicine
Background:
- Coronary artery fistulas (CAFs) are uncommon congenital heart defects.
- Coronary artery-pulmonary artery fistulas can induce myocardial ischemia via coronary steal, stenosis, or vasospasm.
Observation:
- A 73-year-old male presented with a coronary artery-pulmonary artery fistula and significant right coronary artery stenosis.
- Initial diagnostic tests, including myocardial scintigraphy and resting ECG, did not reveal ischemia.
- Exercise ECG suggested coronary steal syndrome due to diffuse ST depression.
Findings:
- Surgical closure of the fistula was complicated by intraoperative coronary spasms and ventricular fibrillation.
- The patient required mechanical circulatory support, including intra-aortic balloon pump and ECMO.
- This case demonstrates that coronary artery fistulas can be associated with vasospasm.
Implications:
- Vasospasm associated with CAFs may be underestimated in preoperative evaluations.
- Thorough preoperative assessment for vasospastic angina is crucial in patients with coronary artery fistulas.
- Understanding this association can improve patient management and surgical outcomes for rare coronary anomalies.
Abstract:
Coronary artery fistulas (CAFs) are rare coronary anomalies. Among these, coronary artery-pulmonary artery fistulas can lead to myocardial ischemia through mechanisms such as coronary steal, stenosis, and vasospasm. We report a case of a 73-year-old male presenting with a coronary artery-pulmonary artery fistula and 75% stenosis of the right coronary artery. Despite negative findings for ischemia on myocardial scintigraphy and the absence of ST changes on a resting electrocardiogram (ECG), coronary steal syndrome was suspected following an exercise ECG that revealed diffuse ST depression. Surgical intervention to close the fistula was performed; however, the patient experienced intraoperative coronary spasms and ventricular fibrillation, necessitating the use of intra-aortic balloon pump and veno-arterial extracorporeal membrane oxygenation. The present case suggested that CAFs can be complicated by vasospasm, which may be overlooked at preoperative diagnostics. In patients with CAFs, careful evaluation regarding vasospastic angina should be done preoperatively.
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