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Isolated left ventricular apical hypoplasia: A case report
Shu-Yi Hu1,2, Chen Meng1,2, Lei-Zhi Ku3
1Department of Cardiology, Wuhan Asia Heart Hospital affiliated to Wuhan University of Science and Technology, Wuhan, Hubei Province, China.
JRSM Cardiovascular Disease
|April 7, 2025
Summary
Isolated left ventricular apical hypoplasia (ILVAH) is a rare cardiomyopathy. Cardiac MRI revealed a truncated LV, apical fat, and right ventricle encirclement, aiding ILVAH diagnosis.
Area of Science:
- Cardiology
- Radiology
- Medical Imaging
Background:
- Isolated left ventricular apical hypoplasia (ILVAH) is a rare, unclassified cardiomyopathy.
- Cardiac magnetic resonance (CMR) is crucial for diagnosing cardiac structural anomalies.
Observation:
- A 32-year-old man presented with sudden dyspnea.
- Multimodal imaging was used to evaluate cardiac structure.
Findings:
- CMR identified significant left ventricular (LV) abnormalities characteristic of ILVAH.
- Observed features included a truncated spherical LV, right ventricle encirclement of the distal LV, and apical fat replacement.
Implications:
- This case highlights the utility of CMR in diagnosing ILVAH.
- Understanding ILVAH's imaging characteristics is vital for accurate diagnosis and management.
Keywords:
Cardiologycomputed tomography and magnetic resonance imagingcoronary angiographycoronary imaging: angiography/ultrasound/Doppler/CCdiagnostic testingtransthoracic echocardiographyMore Related Videos
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