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Chronic granulomatous disease in pregnancy
Obstetrics and Gynecology
|September 1, 1985
Summary
Chronic granulomatous disease impairs phagocyte function, leading to severe infections. This report details the obstetric management for a patient with this rare immune disorder.
Area of Science:
- Immunology
- Obstetrics
- Genetics
Background:
- Chronic granulomatous disease (CGD) is a primary immunodeficiency characterized by impaired phagocytic killing of bacteria.
- Patients with CGD experience recurrent, life-threatening infections, typically presenting in childhood.
- Severe forms of CGD often lead to early mortality, with survival into adulthood being uncommon.