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Pancreatic liposarcoma: A case report.

Yan Zhao1, Shikang Hu2, Huajun Sun3

  • 1Department of Radiology, Sichuan Provincial People's Hospital, University of Electronic Science and Technology of China, Chengdu, Sichuan 610072, P.R. China.

Oncology Letters
|April 16, 2025
PubMed
Summary

Primary pancreatic liposarcoma (LPS) is rare. This case highlights unusual CT findings of dedifferentiated LPS (DDLPS), including vascular invasion and progressive enhancement without fat, aiding diagnosis of this uncommon pancreatic tumor.

Keywords:
CTDDLPSpancreatic LPS

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Area of Science:

  • Oncology
  • Radiology
  • Pathology

Background:

  • Primary liposarcoma (LPS) of the pancreas is an exceptionally rare malignancy.
  • Distinguishing pancreatic tumors requires advanced imaging and pathological analysis.

Observation:

  • A 40-year-old female presented with fever, leading to the discovery of a pancreatic tumor.
  • CT revealed a heterogeneous pancreatic head/body mass with absent fat, vascular encasement, and progressive enhancement.
  • Surgical resection and next-generation sequencing confirmed dedifferentiated LPS (DDLPS).

Findings:

  • The DDLPS case demonstrated atypical CT features: vascular invasion and progressive enhancement without typical fat components.
  • These imaging characteristics presented diagnostic challenges, mimicking other pancreatic neoplasms like neuroendocrine tumors.

Implications:

  • This report provides valuable CT imaging references for diagnosing rare pancreatic DDLPS.
  • Understanding these uncommon manifestations is crucial for accurate differential diagnosis and timely patient management.