Cardiac Juvenile Xanthogranulomatosis in an Infant Presenting With Pericardial Effusion

Mohammad Qasim Mehdi1, Pezad Doctor1, Shannon Kelley2

  • 1Department of Pediatric Cardiology, University of Texas Southwestern, Medical Center, Dallas, Texas, USA.

JACC. Case Reports
|April 18, 2025
PubMed

Insights

Juvenile xanthogranulomatosis can cause large pericardial effusions in infants. This rare condition requires prompt diagnosis and management for better outcomes.

Area of Science:

  • Pediatric Cardiology
  • Pediatric Oncology
  • Neonatal Medicine

Background:

  • Pericardial effusion in infants has diverse etiologies, including infections and tumors.
  • Understanding the underlying cause is crucial for effective management and prognosis.
  • Cardiac tumors are a rare but serious cause of pericardial effusion in neonates and infants.