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Cardiac Juvenile Xanthogranulomatosis in an Infant Presenting With Pericardial Effusion
Mohammad Qasim Mehdi1, Pezad Doctor1, Shannon Kelley2
1Department of Pediatric Cardiology, University of Texas Southwestern, Medical Center, Dallas, Texas, USA.
Insights
Juvenile xanthogranulomatosis can cause large pericardial effusions in infants. This rare condition requires prompt diagnosis and management for better outcomes.
Area of Science:
- Pediatric Cardiology
- Pediatric Oncology
- Neonatal Medicine
Background:
- Pericardial effusion in infants has diverse etiologies, including infections and tumors.
- Understanding the underlying cause is crucial for effective management and prognosis.
- Cardiac tumors are a rare but serious cause of pericardial effusion in neonates and infants.
Abstract:
Understanding the origin of pericardial effusion provides insights on management, risk of recurrence, and outcome. In infants, pericardial effusion can have various causes, including multisystem disease, infection, or cardiac tumors. We describe the case of a previously well 4-month-old infant presenting with a large pericardial effusion secondary to cardiac juvenile xanthogranulomatosis.

