A case of aortitis syndrome with severe coarctation of the aorta

A 17 year old female with aortitis syndrome was reported. The blood pressure of upper extremities was 204/88 mmHg which was higher than that of lower extremities (88/mmHg). Chest X ray showed marked rib notchings at the lower border of the right 7th and 8th rib and left 8th ribs. Stenosis of the thoracic aorta was observed at the upper border of the 9th rib and the lower border of the 10th rib with marked development of collateral circulation. After 6 months treatment with steroids, inflammation signs were improved and thickness of the aorta was decreased which was detected by computed tomography. However, blood pressure was not decreased by the combined antihypertensive treatment.