Sudden cardiac death in an adolescent with unusual coronary artery anomaly

M Holtrup1, L Hernandez1, M Diamond1

  • 1Joe DiMaggio Children's Hospital, Hollywood, FL, USA.

PubMed

Insights

Sudden cardiac death occurred in an adolescent with hypoplastic coronary arteries and myocardial bridging. This rare condition is often missed, necessitating further discussion on preventative treatments.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Sports Cardiology

Background:

  • Hypoplastic coronary arteries and myocardial bridging are rare congenital anomalies.
  • These anomalies can predispose individuals to sudden cardiac death, particularly during physical exertion.
  • Diagnosis can be challenging, often missed in routine evaluations.

Purpose of the Study:

  • To report a case of sudden cardiac death in an adolescent with co-existing hypoplastic coronary arteries and myocardial bridging.
  • To highlight the diagnostic difficulties associated with this rare anomaly.
  • To discuss potential treatment considerations for preventing sudden cardiac death in affected individuals.

Main Methods:

  • Case report presentation.
  • Review of relevant literature on coronary artery anomalies and sudden cardiac death.

Main Results:

  • An adolescent male experienced sudden cardiac death while playing soccer.
  • The patient had a post-mortem diagnosis of hypoplastic coronary arteries and myocardial bridging.
  • This combination of anomalies was not identified prior to the event.

Conclusions:

  • Hypoplastic coronary arteries combined with myocardial bridging represent a high-risk profile for sudden cardiac death in adolescents.
  • Early identification and appropriate management strategies are crucial but challenging.
  • Further research and discussion are needed to establish optimal preventative measures for this rare condition.

Related Concept Videos

Disturbances in Heart Rhythm01:28

Disturbances in Heart Rhythm

Arrhythmia or dysrhythmia refers to an abnormal heart rhythm caused by a defect in the heart's conduction system. It can cause the heart to beat irregularly, too quickly, or too slowly, leading to symptoms like chest pain, shortness of breath, and fainting. Factors such as stress, caffeine, alcohol, nicotine, cocaine, certain drugs, congenital defects, diseases, and electrolyte abnormalities can trigger arrhythmias.
Arrhythmias are categorized by their speed, rhythm, and origin. A slow...
705
Mechanism of Cardiac Arrhythmias01:28

Mechanism of Cardiac Arrhythmias

Arrhythmias are irregular heart rhythms occurring when the heart's electrical impulses become abnormal. These disturbances can lead to various symptoms, depending on their severity and the underlying cause. Some common factors contributing to arrhythmias include hypoxia, ischemia, electrolyte imbalances, excessive catecholamine exposure, drug toxicity, and muscle overstretching. Arrhythmias can be classified into two main types based on the rate and site of origin of abnormal heart rhythms.
849
Ischemic Heart Disease: Overview01:17

Ischemic Heart Disease: Overview

Ischemic heart disease occurs when the heart's blood supply dwindles, causing an ominous lack of oxygen and nutrients. This deficiency, stemming from reduced or obstructed blood flow, spells danger, leading to heart muscle damage and dysfunction.
Atherosclerosis, the primary malefactor, orchestrates this dangerous condition. It manifests as the accumulation of fatty deposits, akin to insidious plaques, within arterial walls. As time elapses, these plaques metamorphose, hardening and...
1.1K
Coronary Circulation01:21

Coronary Circulation

The heart, an organ critical to survival, gets nourishment not from the blood it pumps but from a separate circulation system known as coronary circulation. This is the shortest circulation in the body and is responsible for supplying the heart with the nutrients it needs to function effectively.
Coronary circulation begins at the base of the aorta, where two main arteries arise—the left and right coronary arteries. These arteries encircle the heart in the coronary sulcus and supply the...
1.7K
Cardiovascular System Abnormal Findings II: Auscultation01:25

Cardiovascular System Abnormal Findings II: Auscultation

Auscultation, an essential part of a heart examination, is done using a stethoscope. It provides crucial information about heart function and possible heart problems. Due to heart problems, abnormal sounds can be heard during systole or diastole. These sounds include S3 and S4 gallops, opening snaps, systolic clicks, and murmurs.
Abnormal Heart Sounds
Gallops:
75