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Diagnostic misdirection in posterior-onset Rasmussen's encephalitis: A case report
Rihab Ben Dhia1, Yasmine Saad1, Narjes Gouta1
1Department of Neurology, Fattouma Bourguiba University Hospital, Monastir, Tunisia.
Rasmussen's encephalitis, a rare brain disorder, can initially present solely with occipital seizures. This case highlights the importance of considering this diagnosis in children with drug-resistant visual seizures and cognitive decline.
Area of Science:
- Neurology
- Neuroinflammation
- Pediatric Neurology
Background:
- Rasmussen's encephalitis (RE) is a chronic, progressive inflammatory brain disorder.
- It typically presents with drug-resistant seizures, cognitive decline, and unihemispheric atrophy.
- Focal neurological deficits and motor seizures are common initial symptoms.
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