[MEP-35] Primary Cardiac Tumor: A Case Report of Right Atrial Angiosarcoma

Fatma Akça1, Levent Yazıcıoğlu2, Ali İhsan Hasde2

  • 1Department of Cardiovascular Surgery, Kırıkkale High Specialization Hospital, Kırıkkale, Türkiye.

Insights

Primary cardiac tumors are rare, with angiosarcomas being the most common malignancy. This case highlights the successful surgical resection and reconstruction of a right atrial angiosarcoma, offering long-term survival.

Area of Science:

  • Cardiology
  • Oncology
  • Cardiac Surgery

Background:

  • Primary cardiac tumors are rare, with angiosarcomas being the most common malignant type.
  • Angiosarcomas often occur in the right side of the heart and represent 25-30% of primary cardiac malignancies.
  • Surgical resection is the primary treatment for cardiac angiosarcomas.

Purpose of the Study:

  • To present a case of a 63-year-old female with exertional dyspnea due to a right atrial angiosarcoma.
  • To describe the surgical management and outcomes of primary cardiac angiosarcoma.
  • To emphasize the importance of complete tumor resection for long-term survival.

Main Methods:

  • Diagnosis of an invasive right atrial mass via clinical presentation and imaging.
  • Surgical resection of the angiosarcoma through sternotomy with aortic and venous cannulation.
  • Reconstruction of the right atrial defect using a pericardial patch.

Main Results:

  • Complete resection of the right atrial angiosarcoma was achieved.
  • The patient recovered well and was discharged on postoperative day seven.
  • Postoperative management included chemoradiotherapy.

Conclusions:

  • Surgical resection of primary cardiac angiosarcoma is crucial for achieving long-term survival.
  • Reconstruction of cardiac structures is often necessary after wide tumor resections.
  • Complete tumor removal offers the best prognosis for patients with cardiac angiosarcoma.

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