[MEP-44] Abdominal Aortic Coarctation in an Adolescent Patient

Area of Science:

• Cardiovascular Surgery
• Vascular Medicine
• Genetics

Background:

• A 17-year-old female with neurofibromatosis type 1 presented with hypertension, lymphedema, and dysphagia.
• She had a history of optic glioma and multiple interventions for right renal artery stenosis.
• Radiological examination revealed extensive abdominal aortic coarctation involving multiple visceral arteries.

Purpose of the Study:

• To present a rare case of atypical, long-segment abdominal aortic coarctation.
• To describe the surgical management of complex aortic coarctation in a patient with multiple comorbidities.
• To evaluate the outcomes of surgical repair on hypertension and associated symptoms.

Main Methods:

• A 17-year-old female patient underwent surgical repair for abdominal aortic coarctation.
• The procedure involved patchplasty with a Dacron graft for coarctation involving the SMA and left renal artery.
• Previous interventions included multiple stent balloon procedures and right nephrectomy for renal artery stenosis.

Main Results:

• The patient's severe hypertension resolved postoperatively, with normotension achieved by the seventh day.
• Significant regression of bilateral leg lymphedema was observed after the surgical intervention.
• Dysphagia and postprandial pain, present for four years, were also addressed by the repair.

Conclusions:

• Surgical repair of atypical abdominal aortic coarctation can effectively manage severe hypertension and related symptoms.
• This case highlights the successful treatment of complex vascular anomalies in patients with neurofibromatosis type 1.
• Comprehensive management involving vascular repair can lead to significant improvement in patient quality of life.