Repair of type A aortic dissection in a patient with sickle cell disease
Jake William duPlooy1, Spencer Tingey1, Jorge Seoane1
1Department of Cardiothoracic Surgery, Wake Forest University School of Medicine, 1 Medical Center Blvd, 5th Floor Watlington Hall, Winston-Salem, NC 27157, United States.
We describe a patient with homozygous HbSS sickle cell anemia and end stage renal disease who presented to our medical center with a Stanford type A aortic dissection. His dissection was successfully managed with a hemiarch repair and concomitant bio-Bentall aortic root replacement. Intraoperatively, he received exchange transfusion with omittance of cell saver. Postoperatively, he remained free of sickling events with a very low HbS fraction. His fluid status was managed by continuation of hemodialysis. His hospital course was otherwise uncomplicated, and he was discharged to home on postoperative Day 6.
We describe a patient with homozygous HbSS sickle cell anemia and end stage renal disease who presented to our medical center with a Stanford type A aortic dissection. His dissection was successfully managed with a hemiarch repair and concomitant bio-Bentall aortic root replacement. Intraoperatively, he received exchange transfusion with omittance of cell saver. Postoperatively, he remained free of sickling events with a very low HbS fraction. His fluid status was managed by continuation of hemodialysis. His hospital course was otherwise uncomplicated, and he was discharged to home on postoperative Day 6.


