Multimodality cardiac imaging for pre-operative evaluation in a paediatric criss-cross heart patient: a case report

Kwannapas Saengsin1, Surin Woragidpoonpol2, Tanop Srisuwan3

  • 1Division of Cardiology, Department of Pediatrics, Faculty of Medicine, Chiang Mai University, 110 Inthawarorot Road, Sri Phum Subdistrict, Mueang Chiang Mai District, Chiang Mai 50200, Thailand.

Insights

Criss-cross heart (CCH) is a rare congenital heart disease. Multimodality imaging aids in diagnosing and successfully treating complex CCH cases.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Criss-cross heart (CCH) is an exceptionally rare and complex congenital heart disease (CHD).
  • CCH is characterized by a twisted atrioventricular connection and crossing inflow streams to the ventricles.
  • Accurate diagnosis and treatment planning for CCH are challenging due to its anatomical complexity.

Observation:

  • A one-year-old female presented with cyanosis and abnormal heart sounds.
  • The patient had a complex congenital CCH requiring surgical intervention.
  • Diagnosis and surgical planning were facilitated by advanced imaging techniques.

Findings:

  • Successful biventricular repair was achieved in a patient with complex CCH.
  • Multimodality cardiac imaging, including echocardiography, CT, 3D printing, and 4D flow-CMR, was crucial.
  • This approach enabled precise anatomical assessment and guided the surgical strategy.

Implications:

  • Multimodality cardiac imaging is essential for managing complex congenital heart diseases like CCH.
  • Advanced imaging techniques improve diagnostic accuracy and surgical outcomes in rare CHD.
  • This case highlights the importance of integrated imaging for complex pediatric cardiac conditions.
Abstract

Related Concept Videos

Imaging Studies for Cardiovascular System I:Echocardiography01:17

Imaging Studies for Cardiovascular System I:Echocardiography

Cardiac imaging studies encompass a wide range of noninvasive and minimally invasive techniques designed to visualize the heart's structure and function in detail. One such technique is echocardiography, which uses high-frequency ultrasound waves to produce detailed images of the heart, known as echocardiograms.
Indications: Echocardiography is utilized to diagnose heart failure, valve disorders, and myocardial infarction. It also assesses cardiac structures' size, shape, and motion,...
280
Imaging Studies for Cardiovascular System III: X-Ray01:20

Imaging Studies for Cardiovascular System III: X-Ray

The most common cardiovascular diagnostic test is an X-ray. It produces images of the heart, blood vessels, and adjacent structures.
Definition and Purpose
An X-ray, or radiograph, is a non-invasive method that uses ionizing radiation to take images of internal structures. It is mainly used in cardiac imaging to examine the heart, lungs, and major blood vessels, aiming to identify abnormalities in the heart's size, shape, and position, such as heart failure, congenital defects, and vascular...
118
Imaging Studies for Cardiovascular System II:Types of Echocardiography01:20

Imaging Studies for Cardiovascular System II:Types of Echocardiography

Echocardiography plays a role in assessing cardiac health and detecting heart conditions, with various types providing critical insights for diagnosis and treatment.
Types of Echocardiography
Transthoracic Echocardiography (TTE)
TTE is the most common type of echocardiogram which involves placing a transducer on the patient's chest, emitting sound waves to create heart images. TTE is invaluable for evaluating the heart's size, structure, and motion, making it particularly useful for...
215