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Updated: Sep 19, 2025

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IRE1α-mediated endoplasmic reticulum stress response regulates oxidative damage in CYP4V2 deficient human retinal

Yu-Ting Hsiao1, Chang-Chun Hsiao2, Jong-Jer Lee3

  • 1Department of Ophthalmology, Kaohsiung Chang Gung Memorial Hospital and Chang Gung University College of Medicine, Taiwan; Graduate Institute of Clinical Medical Sciences, College of Medicine, Chang Gung University, Taoyuan, Taiwan; Department of Ophthalmology, Kaohsiung Municipal Feng Shan Hospital-Under the Management of Chang Gung Medical Foundation, Kaohsiung, Taiwan.

Biomedical Journal
|June 4, 2025
PubMed
Abstract

Keywords:
Bietti crystalline dystrophyCYP4V2Endoplasmic reticulum stressInherited retinal diseasesReactive oxygen species

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