Chiari type I malformation with an associated intramedullary schwannoma

A case of Chiari type I malformation associated with a cervical intramedullary schwannoma is presented. A review of the literature concerning intramedullary schwannomas revealed their most frequent location to be in the cervical region. Their optimal treatment seems to be total removal as early in the course as is feasible. Emphasis is given to the need for actual demonstration of the cystic nature of the swollen spinal cord when dealing with Chiari type I malformation.