Related Experiment Video
Updated: Jun 13, 2025

An Immunohistopathologic Study to Profile the Folate Receptor Beta Macrophage and Vascular Immune Microenvironment in Giant Cell Arteritis
Published on: February 8, 2019
The 2025 British Society for Rheumatology management recommendations for ANCA-associated vasculitis
Kathryn Biddle1, Judith Jade2, Harold Wilson-Morkeh3,4
1Department of Rheumatology, Guy's and St Thomas' NHS Foundation Trust, London, UK.
Insights
Updated guidelines offer 26 recommendations for managing ANCA-associated vasculitis (AAV), including granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and eosinophilic granulomatosis with polyangiitis (EGPA), to improve patient care and outcomes.
Area of Science:
- Rheumatology
- Immunology
- Clinical Medicine
Background:
- ANCA-associated vasculitis (AAV) encompasses granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and eosinophilic granulomatosis with polyangiitis (EGPA).
- The previous British Society for Rheumatology (BSR) guideline for AAV management was published in 2014.
- Recent research and clinical trials offer new insights for optimizing AAV patient care and quality of life.
Purpose of the Study:
- To update the 2014 BSR and British Health Professionals in Rheumatology (BHPR) guideline for adult AAV management.
- To provide evidence-based recommendations for AAV treatment and care delivery.
- To incorporate specialist expertise and patient perspectives into AAV management strategies.
Main Methods:
- Systematic literature review of published guidelines and recent research.
- Expert consensus from the BSR AAV Working Group (WG) and UK specialist vasculitis centers.
- Inclusion of patient representatives in the guideline development process.
Main Results:
- A list of 26 updated recommendations for AAV management was formulated.
- Recommendations cover treatment for GPA, MPA, and EGPA, ENT manifestations, service specifications, and patient support.
- Strength of Agreement (SOA) scores were assigned to each recommendation.
Conclusions:
- The updated recommendations provide current evidence and specialist opinion on AAV care delivery.
- The guidelines aim to improve equitable access to care and enhance health outcomes for AAV patients.
- Research and audit recommendations are included to further advance AAV management.
Abstract:
ANCA-associated vasculitis (AAV) is comprised of three specific conditions: granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA) and eosinophilic granulomatosis with polyangiitis (EGPA). Since the publication of the last British Society for Rheumatology (BSR) and British Health Professionals in Rheumatology (BHPR) guideline for the management of adults with AAV in 2014, a plethora of randomized controlled trials, additional research and recommendations have provided novel insights into how the management of AAV can be optimized, thus improving patient quality of life. The BSR AAV Working Group (WG) reviewed published guidelines, undertook a systematic literature review and utilized expertise from specialist vasculitis centres across the UK and patient representatives to formulate a list of 26 recommendations with corresponding strength of agreement (SOA) scores. Recommendations were updated from the published 2014 BSR and BHPR guideline. The 26 recommendations encompassed five key domains: 1. Treatment for GPA and MPA; 2. Management of subglottic stenosis and ear, nose and throat (ENT) manifestations of AAV; 3. Management and treatment for EGPA; 4. Service specifications; 5. Patient education and support. These recommendations provide an update on care delivery of AAV based on current evidence and specialist opinion. In addition, we have provided research and audit recommendations to support equitable access to care and improve health outcomes. The lay summary that accompanies this abstract can be found in Supplementary Data S1, available at Rheumatology online.
Related Concept Videos
Autoimmune Disorders
Concept and Mechanism of Autoimmune Diseases
The immune...
Inflammatory Bowel Disease IV: Pharmacological Management
Pharmacologic...
The JAK-STAT Signaling Pathway

