An unusual case of inflammatory linear verrucous epidermal nevus on the labia majora

Inflammatory linear verrucous epidermal nevus (ILVEN) is a variant of keratinocytic epidermal nevi. In contrast to noninflammatory epidermal naevi, ILVEN is less common, typically erythematous, and persistently pruritic. It usually appears at birth or in early childhood and follows a linear distribution along Blaschko's lines. Genital or perigenital involvement is relatively rare. We report a case of ILVEN on the labia majora of an 11-year-old female. ILVEN usually presents on extremities and trunk, but is uncommon on the genitalia.